National Center for Advancing and Translational Sciences Genetic and Rare Diseases Information Center, a program of the National Center for Advancing and Translational Sciences

Hemangiopericytoma


Categories:
Hemangiopericytoma is a term used to described a group of tumors that are derived from pericytes, the cells normally arranged along specific types of blood vessels called capillaries and venules. These types of tumors are typically slow-growing, may be either benign (non-cancerous) or malignant (cancerous), and may occur anywhere in the body.[1]
Last updated: 11/19/2013

This table lists symptoms that people with this disease may have. For most diseases, symptoms will vary from person to person. People with the same disease may not have all the symptoms listed. This information comes from a database called the Human Phenotype Ontology (HPO) . The HPO collects information on symptoms that have been described in medical resources. The HPO is updated regularly. Use the HPO ID to access more in-depth information about a symptom.

Showing of 27 |
Medical Terms Other Names
Learn More:
HPO ID
5%-29% of people have these symptoms
Fatigue
Tired
Tiredness
[ more ] 		0012378
Neoplasia of the pleura 0100527
Soft tissue neoplasm 0031459
Weight loss 0001824
1%-4% of people have these symptoms
Abnormality of the forehead 0000290
Abnormality of the mediastinum 0045026
Abnormality of the peritoneum 0002585
Constipation 0002019
Diplopia
Double vision
0000651
Fever 0001945
Hypoinsulinemia 0040216
Hypophosphatemic rickets 0004912
Loss of consciousness
Passing out
0007185
Low back pain 0003419
Neoplasm of the liver
Liver cancer
Liver tumor
[ more ] 		0002896
Neoplasm of the lung
Lung tumor
0100526
Neoplasm of the nervous system
Tumor of the nervous system
0004375
Night sweats 0030166
Pelvic mass 0031501
Prostate cancer 0012125
Recurrent hypoglycemia
Recurrent low blood sugar levels
0001988
Reduced C-peptide level 0030795
Urinary retention 0000016
Uterine neoplasm
Uterine tumor
0010784
Vaginal neoplasm
Vaginal tumor
0100650
Percent of people who have these symptoms is not available through HPO
Abnormality of the cardiovascular system
Cardiovascular abnormality
0001626
Autosomal recessive inheritance 0000007
Showing of 27 |
Last updated: 7/1/2020
The cause of the disease is unknown, and no strong clinical data exist to indicate a convincing link to specific causes. Some reports suggest a relationship between hemangiopericytoma and occupational vinyl chloride exposure, as well as exposure to herbicides.[2]
Last updated: 7/9/2013
Radical surgical resection with removal of all meningeal attachments is typically the preferred treatment. However this treatment option is generally possible in only 50-67% of patients who have meningeal hemangiopericytoma. Embolization prior to surgery is recommended because of the excessive bleeding associated with these tumors.[3] Embolization is a method of stopping the blood flow to the tumor. This can be done mechanicially or through the use of chemicals that cause blood vessels to close. If chemicals that kill cells are used during embolization the procedure is referred to as chemoembolization.[2]
Last updated: 11/19/2013

If you need medical advice, you can look for doctors or other healthcare professionals who have experience with this disease. You may find these specialists through advocacy organizations, clinical trials, or articles published in medical journals. You may also want to contact a university or tertiary medical center in your area, because these centers tend to see more complex cases and have the latest technology and treatments.

If you can’t find a specialist in your local area, try contacting national or international specialists. They may be able to refer you to someone they know through conferences or research efforts. Some specialists may be willing to consult with you or your local doctors over the phone or by email if you can't travel to them for care.

You can find more tips in our guide, How to Find a Disease Specialist. We also encourage you to explore the rest of this page to find resources that can help you find specialists.

Healthcare Resources

Research helps us better understand diseases and can lead to advances in diagnosis and treatment. This section provides resources to help you learn about medical research and ways to get involved.

Clinical Research Resources

  • ClinicalTrials.gov lists trials that are related to Hemangiopericytoma. Click on the link to go to ClinicalTrials.gov to read descriptions of these studies.

    Please note: Studies listed on the ClinicalTrials.gov website are listed for informational purposes only; being listed does not reflect an endorsement by GARD or the NIH. We strongly recommend that you talk with a trusted healthcare provider before choosing to participate in any clinical study.

Living with a genetic or rare disease can impact the daily lives of patients and families. These resources can help families navigate various aspects of living with a rare disease.

Financial Resources

These resources provide more information about this condition or associated symptoms. The in-depth resources contain medical and scientific language that may be hard to understand. You may want to review these resources with a medical professional.

In-Depth Information

  • Medscape Reference provides information on this topic. You may need to register to view the medical textbook, but registration is free.
  • The Monarch Initiative brings together data about this condition from humans and other species to help physicians and biomedical researchers. Monarch’s tools are designed to make it easier to compare the signs and symptoms (phenotypes) of different diseases and discover common features. This initiative is a collaboration between several academic institutions across the world and is funded by the National Institutes of Health. Visit the website to explore the biology of this condition.
  • Online Mendelian Inheritance in Man (OMIM) is a catalog of human genes and genetic disorders. Each entry has a summary of related medical articles. It is meant for health care professionals and researchers. OMIM is maintained by Johns Hopkins University School of Medicine. 
  • Orphanet is a European reference portal for information on rare diseases and orphan drugs. Access to this database is free of charge.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Hemangiopericytoma. Click on the link to view a sample search on this topic.

Questions sent to GARD may be posted here if the information could be helpful to others. We remove all identifying information when posting a question to protect your privacy. If you do not want your question posted, please let us know.

  1. Kumar: Robbins and Cotran: Pathologic Basis of Disease, 7th ed.. Saunders, An Imprint of Elsevier; 2005;
  2. Hogle WP. Malignant Hemangiopericytoma. Clinical Journal of Oncology Nursing. January/February 2003;
  3. Kaba SE, Kyritsis AP. Section 10: Neurological Malignancies. Chapter 58: Atypical and Malignant Malinomas. In: Raghavan D, Brecher ML, Johnson DH, Meropol NJ, Moots PL, Rose PG. Textbook of Uncommon Cancer Third Edition. England: John Wiley & Sons, Ltd; 2006;