Congenital self-healing reticulohistiocytosis

Congenital self-healing reticulohistiocytosis is a condition that is a self-limited form of Langerhans cell histiocytosis.[2]: 720 

Congenital self-healing reticulohistiocytosis
Other namesHashimoto–Pritzker disease,[1] and Hashimoto–Pritzker syndrome[2]
SpecialtyDermatology

Symptoms

Non-specific inflammatory response, which includes fever, lethargy, and weight loss. This is suspected of being a genetic disorder, and as the name implies, is self healing.

  • Skin: Commonly seen are a rash which varies from scaly erythematous lesions to red papules pronounced in intertriginous areas. Up to 80% of patients have extensive eruptions on the scalp.
  • Lymph node: Enlargement of the lymph nodes in 50% of Histiocytosis cases.[3]

Diagnosis

History

It was first described by Ken Hashimoto and M. S. Pritzkar in 1973.[4][5]

See also

References
  1. Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 978-1-4160-2999-1.
  2. James, William D.; Berger, Timothy G.; et al. (2006). Andrews' Diseases of the Skin: clinical Dermatology. Saunders Elsevier. ISBN 978-0-7216-2921-6.
  3. "Langerhans Cell Histiocytosis - Patient UK". Retrieved 2007-05-10.
  4. John Thorne Crissey; Lawrence C. Parish; Karl Holubar (2013). Historical Atlas of Dermatology and Dermatologists. CRC Press. p. 179. ISBN 978-1-84214-100-7.
  5. Lee, Young H.; Talekar, Mala K.; Chung, Catherine G.; Bell, Moshe D.; Zaenglein, Andrea L. (February 2014). "Congenital Self-Healing Reticulohistiocytosis". The Journal of Clinical and Aesthetic Dermatology. 7 (2): 49–53. ISSN 1941-2789. PMC 3935651. PMID 24578781.


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