Elastosis perforans serpiginosa

Elastosis perforans serpiginosa
Other names: EPS[1]
Elastosis perforans serpiginosa: Hyperkeratotic plaque of papules[2]

Elastosis perforans serpiginosa is a unique perforating disorder characterized by transepidermal elimination of elastic fibers and distinctive clinical lesions, which are serpiginous in distribution and can be associated with specific diseases.[3][4]

Cause

This dermatological condition is inherited in an autosomal dominant manner.

Histology

Histopathology of this condition

Histopathology of elastosis perforans serpiginosa: Degenerated elastic fibers and transepidermal perforating canals (arrow points at one of them)[2]


Additional images

  • Elastosis perforans serpiginosa
    Elastosis perforans serpiginosa
  • Elastosis perforans serpiginosa
    Elastosis perforans serpiginosa
  • Elastosis perforans serpiginosa
    Elastosis perforans serpiginosa

See also

References

  1. ↑ "OMIM Entry - 130100 - ELASTOSIS PERFORANS SERPIGINOSA; EPS". omim.org. Archived from the original on 28 August 2021. Retrieved 19 April 2019.
  2. 1 2 Hosen, Mohammad J.; Lamoen, Anouck; De Paepe, Anne; Vanakker, Olivier M. (2012). "Histopathology of Pseudoxanthoma Elasticum and Related Disorders: Histological Hallmarks and Diagnostic Clues". Scientifica. 2012: 1–15. doi:10.6064/2012/598262. ISSN 2090-908X.
    -Creative Commons Attribution 3.0 Unported Archived 2011-02-23 at the Wayback Machine license
  3. ↑ Freedberg, et al. (2003). Fitzpatrick's Dermatology in General Medicine. (6th ed.). Page 1041. McGraw-Hill. ISBN 0-07-138076-0.
  4. ↑ Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 978-1-4160-2999-1.
Classification
External resources


This article is issued from Offline. The text is licensed under Creative Commons - Attribution - Sharealike. Additional terms may apply for the media files.